CPQ

Overview

CPQ (carboxypeptidase Q) is a metalloprotease enzyme. It has been newly nominated as a significantly mutated gene in papillary renal cell carcinoma through comprehensive genomic analysis of non-clear-cell RCC.

Alterations observed in the corpus

  • Newly nominated significantly mutated gene in pRCC by multi-method driver analysis; oncogenic vs passenger status unestablished PMID:25401301

Cancer types (linked)

  • PRCC: CPQ identified among new significantly mutated genes in papillary renal cell carcinoma PMID:25401301

Co-occurrence and mutual exclusivity

  • Nominated alongside NF2, SLC5A3, PNKD, LRP2, CHD3, NHERF1, SETD2, and CRTC1 as new significantly mutated genes in pRCC PMID:25401301

Therapeutic relevance

  • No therapeutic relevance established; functional role in pRCC tumorigenesis is unknown PMID:25401301

Open questions

  • Functional characterization of CPQ mutations in cancer is lacking; the authors flag CPQ alongside other newly nominated genes as requiring validation PMID:25401301

Sources

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