IL17RD

Overview

IL17RD (Interleukin 17 Receptor D, also known as SEF) is a negative regulator of FGF receptor signaling and has been described as an inhibitor of the PI3K/AKT pathway through its interaction with FGFR. In adenoid cystic carcinoma (ACC), IL17RD carries a somatic mutation, placing it in the intersection of FGFR and PI3K pathway biology that characterizes a subset of ACC tumors.

Alterations observed in the corpus

  • Mutation observed in adenoid cystic carcinoma (ACC); IL17RD functions as a PI3K inhibitor via FGFR interaction, and its mutation may contribute to PI3K/FGFR pathway dysregulation in ACC PMID:23685749

Cancer types (linked)

  • ACC (adenoid cystic carcinoma): somatic mutation detected in whole-exome sequencing study; functional consequence in ACC not characterized.

Co-occurrence and mutual exclusivity

  • Mutation co-occurs in an ACC genomic landscape dominated by MYB-NFIB fusions and FGFR2 alterations; potential epistatic relationship with FGFR2 mutations not established PMID:23685749

Therapeutic relevance

  • Not directly targeted in the corpus; loss of IL17RD-mediated PI3K inhibition could increase sensitivity to PI3K/AKT inhibitors or FGFR inhibitors in ACC.

Open questions

  • Whether IL17RD mutation results in loss of FGFR-suppressive function and thereby cooperates with FGFR2 activating mutations in ACC has not been tested PMID:23685749

Sources

This page was processed by crosslinker on 2026-05-09.