RIPK4

Overview

RIPK4 (Receptor Interacting Serine/Threonine Kinase 4) is a kinase known to control keratinocyte differentiation. It was nominated as a novel candidate driver in cutaneous squamous cell carcinoma, with mutations clustering in the kinase and ankyrin repeat domains.

Alterations observed in the corpus

  • RIPK4 mutated in 28% of UV-signature aggressive cSCC tumors; mutations clustered in kinase and ankyrin repeat domains; 35% truncating; nominated as a novel candidate driver; known to control keratinocyte differentiation PMID:25303977
  • Squamous-differentiation regulator mutated in 7/29 (24%) metastatic cSCC samples including two truncating mutations; previously reported in head-and-neck SCC PMID:25589618

Cancer types (linked)

  • cSCC — 28% mutation frequency in UV-signature tumors; significant by MutSig/inactivation-bias methods PMID:25303977

Co-occurrence and mutual exclusivity

Therapeutic relevance

Open questions

  • Functional role of RIPK4 mutations in cSCC requires validation; whether mutations are activating or inactivating is not fully established PMID:25303977

Sources

This page was processed by entity-page-writer on 2026-05-11. - PMID:25589618

This page was processed by wiki-cli on 2026-05-14.